Exudative neuroretinopathy and Coats-like response in progressive hemifacial atrophy

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Inferonasal view of the fundus OS displaying the extent of the previews findings.
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Published: Nov 1, 1997
Keywords:
neuroretinopathy, Parry-Romberg syndrome

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Anastasios John Kanellopoulos, MD
Massachusetts Eye and Ear Infirmary, Harvard Medical School; State University of New York at Stony Brook
Fadi Z. El Baba, MD
Massachusetts Eye and Ear Infirmary, Harvard Medical School; State University of New York at Stony Brook
Leslie A. Bruce-Lyle, MD
University of California
Thomas A. Ciulla, MD
Ophthalmic Consultants of Boston, Boston, Massachusetts

Abstract

Progressive hemifacial atrophy (also known as Parry-Romberg syndrome (PRS)), can be associated with ophthalmic manifestations that involve mainly the ipsilateral orbit, adnexae and intraocular structures. We present a patient with typical progressive hemifacial atrophy who demonstrated unusual posterior segment findings. This patient with progressive hemifacial atrophy developed a combination of exudative neuroretinopathy and optic nerve dysfunction resulting in visual loss. Thorough ophthalmologic examination in patients with progressive hemifacial atrophy (PRS) is essential.

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How to Cite
1.
Kanellopoulos AJ, El Baba FZ, Bruce-Lyle LA, Ciulla TA. Exudative neuroretinopathy and Coats-like response in progressive hemifacial atrophy. Digit J Ophthalmol. 1997;3(4). Accessed May 15, 2026. https://djo.harvard.edu/index.php/djo/article/view/948
Issue
Vol. 3 No. 4 (1997)
Section
Original Articles
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This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.

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