Endothelial dysfunction in a child with Pearson marrow-pancreas syndrome managed with Descemet stripping automated endothelial keratoplasty using a suture pull-through technique

Raghav Vadhul, BS; Caroline S. Halbach, MD; Raymond G. Areaux Jr., MD; Susan Berry, MD; Joshua H. Hou, MD

doi:10.5693/djo.02.2019.09.001

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Published: Nov 17, 2019

DOI: https://doi.org/10.5693/djo.02.2019.09.001

Raghav Vadhul, BS

Indiana University School of Medicine, Indianapolis, Indiana

Caroline S. Halbach, MD

Department of Ophthalmology and Visual Neurosciences, University of Minnesota, Minneapolis, Minnesota

Raymond G. Areaux Jr., MD

Department of Ophthalmology and Visual Neurosciences, University of Minnesota, Minneapolis, Minnesota

Susan Berry, MD

Department of Pediatrics, University of Minnesota, Minneapolis, Minnesota

Joshua H. Hou, MD

Department of Ophthalmology and Visual Neurosciences, University of Minnesota, Minneapolis, Minnesota

Abstract

A 4-year-old girl with a history of Pearson marrow-pancreas syndrome presenting with severe, progressive photophobia was found to have bilateral, diffuse corneal thickening and peripheral pigmentary retinopathy. She underwent Descemet stripping automated endothelial keratoplasty (DSAEK) surgery in both eyes using a modified suture pull-through technique. Postoperatively there was no evidence of cataract formation or graft detachment; her corneas thinned, and her photophobia improved dramatically.

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Vadhul, BS R, Halbach, MD CS, Areaux Jr., MD RG, Berry, MD S, Hou, MD JH. Endothelial dysfunction in a child with Pearson marrow-pancreas syndrome managed with Descemet stripping automated endothelial keratoplasty using a suture pull-through technique. Digit J Ophthalmol. 2019;25(4):59-64. doi:10.5693/djo.02.2019.09.001

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Vol. 25 No. 4 (2019)

Section

Case Reports

This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.

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