Cogan syndrome: a case report and review of the literature

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Slit lamp photograph showing inflammation and crystalline deposits on the corneal stroma.
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Published: Sep 14, 2023
DOI: https://doi.org/10.5693/djo.02.2023.07.001
Keywords:
Corneal opacification, Interstitial keratitis, Hearing loss, Cogan’s syndrome

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Nicolás Kahuam-López, MD
Department of Cornea and Refractive Surgery, Instituto de Oftalmología “Conde de Valenciana,” Mexico City, Mexico
https://orcid.org/0000-0003-3887-0629
Guillermo R. Vera-Duarte, MD
Department of Cornea and Refractive Surgery, Instituto de Oftalmología “Conde de Valenciana,” Mexico City, Mexico
https://orcid.org/0000-0002-3417-256X
Ana Karen Pérez-Vázquez, MD
bCentro de Investigación en Ciencias de la Salud (CICSA), Facultad de Ciencias de la Salud, Universidad Anáhuac México, Campus Norte, Huixquilucan, Mexico
https://orcid.org/0000-0002-8138-678X
Alejandro Navas, MD, PhD
Department of Cornea and Refractive Surgery, Instituto de Oftalmología “Conde de Valenciana,” Mexico City, Mexico
https://orcid.org/0000-0002-9417-5711
Arturo Ramirez-Miranda, MD, MSc
Department of Cornea and Refractive Surgery, Instituto de Oftalmología “Conde de Valenciana,” Mexico City, Mexico
https://orcid.org/0000-0001-6419-5116
Enrique O. Graue-Hernandez, MD, MSc
Department of Cornea and Refractive Surgery, Instituto de Oftalmología “Conde de Valenciana,” Mexico City, Mexico
https://orcid.org/0000-0003-3267-3915

Abstract

Cogan syndrome is a rare disease whose etiology is still undetermined. It typically affects men and women between the second and fourth decade of life. We report a case of Cogan syndrome with ocular and audio-vestibular involvement as a systemic manifestation in a 31-year-old woman.

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How to Cite
1.
Kahuam-López N, Vera-Duarte GR, Pérez-Vázquez AK, Navas A, Ramirez-Miranda A, Graue-Hernandez EO. Cogan syndrome: a case report and review of the literature. Digit J Ophthalmol. 2023;29(3):88-93. doi:10.5693/djo.02.2023.07.001
Issue
Vol. 29 No. 3 (2023)
Section
Case Reports
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This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.

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